Ebstein anomaly is a congenital malformation of the heart that is characterized by apical displacement of the septal and posterior tricuspid valve leaflets, leading to atrialization of the right ventricle with a variable degree of malformation and displacement of the anterior leaflet. Treatment of Ebstein anomaly is complex and dictated mainly by the severity of the disease itself and the effect of accompanying congenital structural and electrical abnormalities. Treatment options include medical therapy, radiofrequency ablation, and surgical therapy. The case report tells us that Mr. y 22yrsold man with Ebstein anomlypresented with a complaints ofexercise is intolerance, Cyanosis, Fatigue and dyspnea since 2 months. On examination widely split first heart sound with loud tricuspid component and soft/absent mitral component in the presence of prolonged PR interval; usually normal second heart sound but may be widely split when pulmonary component delayed due to right bundle-branch block; third and fourth heart sounds commonly present, even in the absence of congestive heart failure. Patient was under the treatment of medical management.